Anaesthetic Management with Thromboelastography in a Patient with Glanzmann Thrombasthenia.

نویسندگان

  • Ahmet Topal
  • Alper Kılıçaslan
  • Atilla Erol
  • Barış Çankaya
  • Şeref Otelcioğlu
چکیده

Glanzmann thrombastenia (GT) is a rare disease of an autosomal recessive inheritance characterized with fatal bleeding tendency. The anaesthesiologist should be cognizant of the risk involved and be prepared with necessary measures. In this paper, we present a GT case of a 9-year-old male with hypospadias, which was successfully repaired after platelet transfusions according to the thromboelastography tracings.

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عنوان ژورنال:
  • Turkish journal of anaesthesiology and reanimation

دوره 42 4  شماره 

صفحات  -

تاریخ انتشار 2014